Primary Small Cell Neuroendocrine Carcinoma of Larynx: An Atypical Case Presentation

Neuroendocrine tumors account for <1% of all malignant tumors that can originate from any part of the body, most frequently diagnosed in the lung. Extrapulmonary presentation is rare, common sites are genitourinary and gastrointestinal. According to the 2017 WHO proposed classification, small cell type (SCNEC) is a poorly differentiated neuroendocrine carcinoma. The most common site in the head and neck is the larynx, accounts for <0.6%. Small cell neuroendocrine carcinomas are extremely rare entity of laryngeal cancers. We report a case of small cell neuroendocrine carcinoma of larynx.